No | Group (first author) | Age/sex | Site/number | Malignant manifestations | Associated tumors | Associated jaundice | Procedure performed | Follow up |
---|---|---|---|---|---|---|---|---|
1 | Compagno, 1978 [7] | NA | 3 cases | No | No | Yes | ||
2 | SCA-diffuse | (One case) | ||||||
3 | NA | NA | ||||||
4 | Shorten, 1986 [15] | 60/F | SCA–diffuse | No | No | No | Core needle biopsy only | A & W, 2 yr |
5 | Kim, 1990 [16] | 32/F | SCA–diffuse | No | No | No | Subtotal pancreatectomy | A & W 3 months |
6 | Kim, 1997 [17] | 67/F | SCA–diffuse | No | Pancreatic endocrine tumor | No | Whipple’s procedure | NA |
7 | Yasuhara, 2002 [18] | 51/M | SCA–diffuse | No | No | No | Total pancreatectomy | A & W 3 months |
8 | Tampi, 2006 [19] | 36/F | SCA–diffuse | No | No | No | Subtotal pancreatectomy | NA |
9 | Agarwal, 2009 [20] | 35/F | SCA–diffuse | No | Neuroendocrine carcinoma | No | Total pancreatectomy | NA |