Ohara et al. | Kusaba et al. | Patient 1 | Patient 2 | |
---|---|---|---|---|
Age, sex | 13, M | 59, F | 12, M | 24, F |
Underlying disease | Short bowel syndrome | Post-radiation enteritis | MMIHS | MMIHS |
Duration of CVC (years) | 13 | 2 | 8 | 18 |
Blood culture | S. epidermidis | S. epidermidis | S. epidermidis (MSSE) | S. epidermidis (MRSE) |
24 h CCr/e-GFR (mL/min/1.73 m2) | 84.6/− | −/5.3 | 77.4/70.8 | −/63.1 |
C3/C4/CH50 | 30/8/ <10 | 30/10/ <12 | 69/7.4/26.4 | 57/24/10.5 |
PR3-ANCA | N/D | <5 | 33 | 19 |
Renal pathology (positive IF) | MPGN C3, IgM, C1 | Crescentic GN C3, IgM, IgG | MPGN C3, IgM, C1q | MPGN C3, IgM |
Treatment | CVC removal | CVC removal | CVC removal | CVC removal |
Cefazolin for 10 days | Cefazolin (3 g/day) for 10 days | Cefazolin (3 g/day) for 7 days | ||
PSL 60 mg/day + MZR 150 mg/day for 10 days | MPT 2 courses + PSL 40 mg/day for 1 month | |||
Outcome | Full recovery | ESRD | Full recovery | Full recovery |