Variables | Mean ± SD | Value range | Number of observations | |
---|---|---|---|---|
Age (years) | 17.9 ± 10.6 | 5–57 | 484 | |
Haematological indices | RBC (1012/l) | 2.8 ± 0.7 | 1.2–5.5 | 484 |
Hb (g/dl) | 7.8 ± 1.6 | 4.0–13.5 | 484 | |
MCV(fl) | 84.6 ± 10.0 | 61–112 | 484 | |
MCHC (g/dl) | 34.2 ± 3.8 | 22.3–54.0 | 484 | |
WBC (109/l) | 14.7 ± 6.4 | 3.5–48.8 | 484 | |
Lymphocytes (109/l) | 6.1 ± 3.3 | 0.87–20.4 | 484 | |
Monocytes (109/l) | 1.7 ± 1.4 | 0.1–10.9 | 484 | |
Platelets (109/l) | 371.5 ± 131.6 | 108–827 | 484 | |
HbA2 (%) | 3.6 ± 2.1 | 0.1–18.2 | 484 | |
HbF (%) | 10.1 ± 8.5 | 0–37.4 | 484 | |
Clinical events | Vaso-occlusive crisis (No./year) | 2.8 ± 3.3 | 0–40 | 484 |
Consultations (No./year) | 3.0 ± 3.9 | 0–24 | 484 | |
Hospitalisation (No./year) | 1.4 ± 2.5 | 0–30 | 484 | |
Overt stroke | 4.5% | 22/484 | ||
3.7del α-globin gene genotypes | αα/αα | 62.9% | 304/484a | |
αα/α3.7 | 28.5% | 138/484a | ||
α3.7/α3.7 | 8.6% | 42/484a | ||
β-globin gene haplotypes | Benin/Benin | 50.2% | 243/484a | |
Benin/Cameroon | 21.7% | 105/484a | ||
Benin/Atypical | 4.1% | 20/484a | ||
Cameroon/Cameroon | 4.1% | 20/484a |