Characteristics | n (%); mean ± SD (normal range) |
---|---|
Gender | |
Male | 14 (54) |
Female | 12 (46) |
Age at diagnosis (days) | 126 ± 77.9 |
Biliary atresia type | |
Type 1 | 0 |
Type 2a | 6 (23) |
Type 2b | 2 (8) |
Type 3 | 18 (69) |
Pre-operative body weight (kg) | 5.5 ± 2.4 |
Pre-operative laboratory findings | |
Total bilirubin (mg/dL) | 10.8 ± 5.4 (≤ 1.0) |
Direct bilirubin (mg/dL) | 8.4 ± 2.7 (0–0.2) |
Alanine aminotransferase (ALT) (U/L) | 140 ± 75.1 (≤ 41) |
Aspartate aminotransferase (AST) (U/L) | 231.7 ± 98.0 (≤ 40) |
Alkaline phosphatase (ALP) (U/L) | 568.5 ± 249.8 (≤ 462) |
Gamma glutamyl transferase (GGT) (U/L) | 544.4 ± 341.9 (7–64) |
Albumin (g/dL) | 3.3 ± 0.6 (3.9–4.9) |
International normalized ratio (INR) | 1.9 ± 1.6 (0.9–1.1) |
White blood cells (×103/μL) | 13.9 ± 8.3 (4.5–13.5) |
Neutrophil (%) | 41.0 ± 14.1 (35.0–65.0) |
Lymphocyte (%) | 42.5 ± 19.4 (23.0–53.0) |
Pre-operative portal hypertension features | |
Esophageal varices | 3 (12) |
Splenomegaly | 10 (38) |
Platelet (×103/μL) | 315.4 ± 176.8 (150–450) |
Ascites | 15 (58) |
Age at Kasai procedure performed (days) | |
< 60 | 2 (8) |
≥ 60 | 24 (92) |
Histopathological findings of liver biopsy | |
Liver cirrhosis | 11 (42) |
Non-liver cirrhosis | 15 (58) |
Sonography findings | |
Undetectable gallbladder | 11 (42) |
Triangular cord sign | 5 (19) |
Outcomes | |
Survived | 15 (58) |
Died | 11 (42) |
Cause of death | |
Septic shock | 2 (18) |
Pulmonary edema | 2 (18) |
Hemorrhagic shock | 1 (9) |
Aspiration pneumonia | 2 (18) |
Hepatopulmonary syndrome | 1 (9) |
Multiple organ dysfunction syndrome | 3 (27) |
Characteristics | Liver transplant score | p value | OR (95% CI) | |
---|---|---|---|---|
< 8 | ≥ 8 | |||
Gender | ||||
Male | 6 | 8 | 0.23 | 2.7 (0.5–13.2) |
Female | 8 | 4 | ||
Age at Kasai procedure performed (days) | ||||
≥ 60 | 12 | 12 | 0.31 | 5.0 (0.2–115.1) |
< 60 | 2 | 0 |